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277.87 - Disorders Of Mitochondrial Metabolism


The ICD 9 Code for Disorders of mitochondrial metabolism is listed as 277.87.
Additional information concerning this code and description can be found below including ICD 10 crosswalks / GEMS, and chapter information where available.
ICD 9 CM Field Value
Diagnosis Code: 277.87
Long Description: Disorders of mitochondrial metabolism
Short Description: Dis mitochondrial metab
Chapter: Endocrine, Nutritional And Metabolic Diseases, And Immunity Disorders
Block: Other Metabolic Disorders And Immunity Disorders (270-279)
Related Descriptions: Juvenile myopathy, encephalopathy, lactic acidosis AND stroke
Kearns-Sayre syndrome
Mitochondrial encephalomyopathy
Myoclonus epilepsy AND ragged red fibers
Neurogenic muscle weakness, ataxia and retinitis pigmentosa
Pearson's syndrome
ICD-10-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD-10-CM Code: E88.40 - Mitochondrial metabolism disorder, unspecified (approximate)
ICD-10-CM Code: E88.41 - MELAS syndrome (approximate)
ICD-10-CM Code: E88.42 - MERRF syndrome (approximate)
ICD-10-CM Code: E88.49 - Other mitochondrial metabolism disorders (approximate)
ICD-10-CM Code: H49.819 - Kearns-Sayre syndrome, unspecified eye (approximate)
ICD-9-CM Siblings (same level / similar specificity) of 277.87:
277.81 - Primary carnitine deficiency
277.82 - Carnitine deficiency due to inborn errors of metabolism
277.83 - Iatrogenic carnitine deficiency
277.84 - Other secondary carnitine deficiency
277.85 - Disorders of fatty acid oxidation
277.86 - Peroxisomal disorders
277.88 - Tumor lysis syndrome
277.89 - Other specified disorders of metabolism