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H49.81 - Kearns-Sayre syndrome


The ICD 10 Code for Kearns-Sayre syndrome is listed as H49.81.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: H49.81
Description: Kearns-Sayre syndrome
  • Progressive external ophthalmoplegia with pigmentary retinopathy
  • Use additional code for other manifestation, such as:
  • heart block (I45.9)
Chapter Diseases of the eye and adnexa (H00-H59)
Block Disorders of ocular muscles, binocular movement, accommodation and refraction (H49-H52)
Parent H49.8 - Other paralytic strabismus
ICD-10-CM Children (deeper level / typically more specific) of H49.81:
H49.811 - Kearns-Sayre syndrome, right eye
H49.812 - Kearns-Sayre syndrome, left eye
H49.813 - Kearns-Sayre syndrome, bilateral
H49.819 - Kearns-Sayre syndrome, unspecified eye
ICD-10-CM Siblings (same level / similar specificity) of H49.81:
H49.88 - Other paralytic strabismus