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E88.4 - Mitochondrial metabolism disorders


The ICD 10 Code for Mitochondrial metabolism disorders is listed as E88.4.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: E88.4
Description: Mitochondrial metabolism disorders
  • Excludes1: disorders of pyruvate metabolism (E74.4)
  • Kearns-Sayre syndrome (H49.81)
  • Leber's disease (H47.22)
  • Leigh's encephalopathy (G31.82)
  • Mitochondrial myopathy, NEC (G71.3)
  • Reye's syndrome (G93.7)
Chapter Endocrine, nutritional and metabolic diseases (E00-E89)
Block Metabolic disorders (E70-E88)
Parent E88 - Other and unspecified metabolic disorders
ICD-10-CM Children (deeper level / typically more specific) of E88.4:
E88.40 - Mitochondrial metabolism disorder, unspecified
E88.41 - MELAS syndrome
E88.42 - MERRF syndrome
E88.49 - Other mitochondrial metabolism disorders
ICD-10-CM Siblings (same level / similar specificity) of E88.4:
E88.0 - Disorders of plasma-protein metabolism, not elsewhere classified
E88.1 - Lipodystrophy, not elsewhere classified
E88.2 - Lipomatosis, not elsewhere classified
E88.3 - Tumor lysis syndrome
E88.8 - Other specified metabolic disorders
E88.9 - Metabolic disorder, unspecified