eMedCodes logo

E74.4 - Disorders of pyruvate metabolism and gluconeogenesis


The ICD 10 Code for Disorders of pyruvate metabolism and gluconeogenesis is listed as E74.4.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: E74.4
Description: Disorders of pyruvate metabolism and gluconeogenesis
  • Deficiency of phosphoenolpyruvate carboxykinase
  • Deficiency of pyruvate carboxylase
  • Deficiency of pyruvate dehydrogenase
  • Excludes1: disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
  • Leigh's syndrome (G31.82)
Diagnostic Related Groups
(MS-DRG v30.0)
642 - Inborn And Other Disorders Of Metabolism
Chapter Endocrine, nutritional and metabolic diseases (E00-E89)
Block Metabolic disorders (E70-E88)
Parent E74 - Other disorders of carbohydrate metabolism
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 271.0 - Other specified disorders of carbohydrate transport and metabolism (approximate)
ICD 9 Dx Code: 271.8 - Other specified disorders of carbohydrate transport and metabolism (approximate)
ICD-10-CM Siblings (same level / similar specificity) of E74.4:
E74.0 - Glycogen storage disease
E74.1 - Disorders of fructose metabolism
E74.2 - Disorders of galactose metabolism
E74.3 - Other disorders of intestinal carbohydrate absorption
E74.8 - Other specified disorders of carbohydrate metabolism
E74.9 - Disorder of carbohydrate metabolism, unspecified