E71.0 - Maple-syrup-urine disease
The ICD 10 Code for Maple-syrup-urine disease is listed as E71.0.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.
| ICD 10 CM Field | Value |
|---|---|
| Diagnosis Code: | E71.0
|
| Description: | Maple-syrup-urine disease |
| Diagnostic Related Groups
(MS-DRG v30.0) |
642 - Inborn And Other Disorders Of Metabolism
|
| Chapter | Endocrine, nutritional and metabolic diseases (E00-E89) |
| Block | Metabolic disorders (E70-E88) |
| Parent | E71 - Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism |
| ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS): | |
| ICD 9 Dx Code: | 270.3 - Disturbances of branched-chain amino-acid metabolism (approximate) |
| ICD-10-CM Siblings (same level / similar specificity) of E71.0: | |
| E71.1 - Other disorders of branched-chain amino-acid metabolism | |
| E71.2 - Disorder of branched-chain amino-acid metabolism, unspecified | |
| E71.3 - Disorders of fatty-acid metabolism | |
| E71.4 - Disorders of carnitine metabolism | |
| E71.5 - Peroxisomal disorders | |