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D81.81 - Biotin-dependent carboxylase deficiency


The ICD 10 Code for Biotin-dependent carboxylase deficiency is listed as D81.81.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: D81.81
Description: Biotin-dependent carboxylase deficiency
  • Multiple carboxylase deficiency
  • Excludes1: biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
Chapter Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block Certain disorders involving the immune mechanism (D80-D89)
Parent D81.8 - Other combined immunodeficiencies
ICD-10-CM Children (deeper level / typically more specific) of D81.81:
D81.810 - Biotinidase deficiency
D81.818 - Other biotin-dependent carboxylase deficiency
D81.819 - Biotin-dependent carboxylase deficiency, unspecified
ICD-10-CM Siblings (same level / similar specificity) of D81.81:
D81.89 - Other combined immunodeficiencies