D81.6 - Major histocompatibility complex class I deficiency

The ICD 10 Code for Major histocompatibility complex class I deficiency is listed as D81.6.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field	Value
Diagnosis Code:	D81.6
Description:	Major histocompatibility complex class I deficiency Bare lymphocyte syndrome
Diagnostic Related Groups (MS-DRG v30.0)	808 - Major Hematol/immun Diag Exc Sickle Cell Crisis & Coagul W Mcc 809 - Major Hematol/immun Diag Exc Sickle Cell Crisis & Coagul W Cc 810 - Major Hematol/immun Diag Exc Sickle Cell Crisis & Coagul W/o Cc/mcc

Chapter	Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block	Certain disorders involving the immune mechanism (D80-D89)
Parent	D81 - Combined immunodeficiencies
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code:	279.2 - Combined immunity deficiency (approximate)
ICD-10-CM Siblings (same level / similar specificity) of D81.6:
D81.0 - Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1 - Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2 - Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3 - Adenosine deaminase [ADA] deficiency
D81.4 - Nezelof's syndrome
D81.5 - Purine nucleoside phosphorylase [PNP] deficiency
D81.7 - Major histocompatibility complex class II deficiency
D81.8 - Other combined immunodeficiencies
D81.9 - Combined immunodeficiency, unspecified