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C96.0 - Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis


The ICD 10 Code for Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis is listed as C96.0.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: C96.0
Description: Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis
  • Histiocytosis X, multisystemic
  • Letterer-Siwe disease
  • Excludes1: adult pulmonary Langerhans cell histiocytosis (J84.82)
  • multifocal and unisystemic Langerhans-cell histiocytosis (C96.5)
  • unifocal Langerhans-cell histiocytosis (C96.6)
Diagnostic Related Groups
(MS-DRG v30.0)
011 - Tracheostomy For Face,mouth & Neck Diagnoses W Mcc
012 - Tracheostomy For Face,mouth & Neck Diagnoses W Cc
013 - Tracheostomy For Face,mouth & Neck Diagnoses W/o Cc/mcc
826 - Myeloprolif Disord Or Poorly Diff Neopl W Maj O.r. Proc W Mcc
827 - Myeloprolif Disord Or Poorly Diff Neopl W Maj O.r. Proc W Cc
828 - Myeloprolif Disord Or Poorly Diff Neopl W Maj O.r. Proc W/o Cc/mcc
829 - Myeloprolif Disord Or Poorly Diff Neopl W Other O.r. Proc W Cc/mcc
830 - Myeloprolif Disord Or Poorly Diff Neopl W Other O.r. Proc W/o Cc/mcc
843 - Other Myeloprolif Dis Or Poorly Diff Neopl Diag W Mcc
844 - Other Myeloprolif Dis Or Poorly Diff Neopl Diag W Cc
845 - Other Myeloprolif Dis Or Poorly Diff Neopl Diag W/o Cc/mcc
Chapter Neoplasms (C00-D49)
Block Malignant neoplasms of lymphoid, hematopoietic and related tissue (C81-C96)
Parent C96 - Other and unspecified malignant neoplasms of lymphoid, hematopoietic and related tissue
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 202.50 - Letterer-siwe disease, unspecified site, extranodal and solid organ sites (approximate)
ICD-10-CM Siblings (same level / similar specificity) of C96.0:
C96.2 - Malignant mast cell tumor
C96.4 - Sarcoma of dendritic cells (accessory cells)
C96.5 - Multifocal and unisystemic Langerhans-cell histiocytosis
C96.6 - Unifocal Langerhans-cell histiocytosis
C96.9 - Malignant neoplasm of lymphoid, hematopoietic and related tissue, unspecified
C96.A - Histiocytic sarcoma
C96.Z - Other specified malignant neoplasms of lymphoid, hematopoietic and related tissue